Dermatomyositis presenting as periorbital edema

PReS-FINAL-2285: Pediatric non-renal SLE presenting as periorbital edema: response to treatment with belimumab

Methods Case report: A 16 year old white female presented with a three month history of periorbital edema in the setting of positive lupus serologies, synovitis, and hypocomplementemia. She had failed treatment with anti-histamines and had responded well to the use of oral steroids, but her symptoms quickly recurred upon tapering off steroids. Over the following six months, treatment with hydro...

Periorbital and facial swelling due to dermatomyositis.

Localized periorbital edema as a clinical manifestation of sulfite sensitivity.

Sulfite is commonly used in pharmaceuticals as a preservative. We report a unique clinical presentation of localized periorbital edema on the left eye after administration of sulfite-containing dexamethasone. The patient's sulfite sensitivity was confirmed by sulfite oral provocation test: periorbital edema on the same site developed after ingestion of 200 mg sodium bisulfite. She was non-atopi...

Periorbital edema as initial manifestation of chronic cutaneous lupus erythematosus

Periorbital edema occurs frequently in dermatomyositis, but it has rarely been noted in systemic systemic lupus erythematosus. We describe a patient who developed bilateral periorbital edema and erythema as the sole manifestation of systemic lupus erythematosus.

Paraneoplastic Dermatomyositis Syndrome Presenting as Dysphagia

Dermatomyositis (DM) is a rare autoimmune condition which predominantly affects females in the fifth and sixth decades of life. DM presents acutely or progressively as painless proximal skeletal muscle weakness and can be associated with a heliotropic rash around the eyes, and Gottron's papules on extensor surfaces of the hands. While the pathophysiology of DM is still unclear, abnormal T- and ...